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KMID : 0358920220490020234
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Journal of the Korean Academy of Pedodontics
2022 Volume.49 No. 2 p.234 ~ p.240
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Dental and Skeletal Characteristics and Behavioral Aspects of the Patient with Floating-Harbor Syndrome Compared with Twin Sister
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Lim Jong-Hwa
Kim Gi-Min
Lee Jae-Sik
Nam Soon-Hyeun
Kim Hyun-Jung
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Abstract
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Floating-Harbor syndrome (FHS) is a rare genetic disorder. This report introduced in a patient with FHS. Distinctive facial characteristics, severe skeletal class 3 malocclusion with underdeveloped maxilla and protruded mandible, congenital missing teeth, microdontia and ectopic positions of maxillary teeth were presented in the patient. In his twin sister, mild skeletal class 3 malocclusion with protruded mandible was observed but congenital missing teeth and microdontia were not observed. High-arched palate, narrow V-shaped maxillary arch compared to wide and ovoid mandibular arch and inverse relationship between the maxillary and mandibular intermolar width resulted in posterior crossbite were confirmed by model analysis of the patient. These were not observed in the twins. Behaviorally, poor cooperation during dental treatment because of mental retardation was observed in the patient.
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KEYWORD
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Floating-Harbor syndrome, Dental and skeletal characteristics, Behavioral aspects, Twins
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